Title of article
SHWACHMAN SYNDROME. REPORT OF THREE CASES
Author/Authors
Farhoudi, A Tehran Universtiy of Medical Sciences , Atarod, L Tehran Universtiy of Medical Sciences , Mirsaid Ghazi, B Tehran Universtiy of Medical Sciences
Pages
7
From page
89
To page
95
Abstract
Shwachman syndrome, next to cystic fibrosis, is the second cause of congenita! exocrine pancreatic insufficiency in children. It appears as steatorrhea, recurrent infections and hematologic abnormalities such as neutropenia, skeletal dysplasia and short stature. In this study, we reviewed 3 patients’ histories. All of them showed cellular chemotaxic defect. One of them had been affected by nephrotic syndrome and finally succumbed to septic shock. This patient suffered from skeletal disorders.
Keywords
Shwachman Syndrome , Chemotaxis , Nephrotic Syndrome
Journal title
Astroparticle Physics
Serial Year
2000
Record number
2434496
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