Title of article
Congenital Hypofibrinogenemia Detected during Preoperative Workup for Major Cardiac Surgery
Author/Authors
Chetak, KB Department of Pediatrics - Jss Medical College - Jss Academy of Higher Education and Research - Mysore, India , Kumar, K Jagadish Department of Pediatrics - Jss Medical College - Jss Academy of Higher Education and Research - Mysore, India , Hiremath, Vilas Coagulation Specialist - Vijayashree Diagnostics - Cross - 3rd Block Koramangala Bangalore , Sujay, KR Jss Medical College - Jss Academy of Higher Education and Research - Mysore, India , Dinesh Kumar, US Jss Medical College - Jss Academy of Higher Education and Research - Mysore, India
Pages
3
From page
96
To page
98
Abstract
Afibrinogenemia or hypofibrinogenemia is a quantitative defect in fibrinogen. It
is a rare disease with estimated frequency of 1 in 1,000,000 population. Routine
preoperative screening tests of coagulation disorders are insufficient to detect
subtle disorders of fibrinogen. Herein, we report a child who was supposed
to undergo open cardiac surgery for a large atrial septal defect. Preoperative
coagulation screening tests revealed minimal prolongation of prothrombin
time which made us do further work-up. Finally, she was diagnosed with
hypofibrinogenemia who was suggested to be congenital.
Keywords
Thrombin time , Congenital hypofibrinogenemia , Afibrinogenemia Cardiac surgery , Coagulation screening tests , Prolonged prothrombin time
Journal title
Astroparticle Physics
Serial Year
2018
Record number
2481170
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