Title of article
Amyloidosis as a Renal Complication of Chronic Granulomatous Disease
Author/Authors
Darougar, Sepideh Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Rashid Farokhi, Farin Tehran University of Medical Sciences, Tehran, Iran , Tajik, Shaghayegh Tehran University of Medical Sciences, Tehran, Iran , Baghaie, Nooshin Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Amirmoini, Mehrdad Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Bashardoust, Bahram Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Hashemitari, Karen Tehran University of Medical Sciences, Tehran, Iran , Mahdaviani, Alireza Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran
Pages
5
From page
228
To page
232
Abstract
Chronic granulomatous disease is a rare primary immunodeficiency
disorder, which leads to increased susceptibility to recurrent
infections and severe inflammatory manifestations. There have been
reports regarding different aspects of genitourinary involvement in
chronic granulomatous disease, some of which are hydronephrosis,
granulomatous cystitis, and glomerulonephritis, but among these
complications, amyloidosis is rather rare. We report a patient with
chronic granulomatous disease that developed amyloidosis later
in the course of the disease.
Keywords
amyloidosis , genitourinary involvement , chronic granulomatous disorder
Journal title
Iranian Journal of Kidney Diseases (IJKD)
Serial Year
2016
Record number
2519374
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