Multiple familial trichoepitheliomas

Trichoepithelioma (TE) is a benign cutaneous tumor that originates from hair follicles and occurs either in multiple or solitary forms. Multiple familial trichoepitheliomas (MFT) is transmitted as an autosomal dominant trait, and a region at 9p21 is thought to be involved in the tumorigenesis. Solitary TE occurs more commonly than multiple TE, is not inherited and rarely seen in perianal region. We present a family with MFT, of which several members; both male and female were affected. The tumor is benign but is important to recognize because of histopathological significance