Title of article
Ectrodactyly-Ectodermal Dysplasia-Clefting Syndrome: Report of a Case with Oral Manifestations
Author/Authors
Taheri, Jamile Bigom shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Azimi, Somayyeh shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Mortazavi, Hamed shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Babaee, Somayyeh shahid beheshti university of medical sciences - School of Dentistry - Department of Oral Medicine, تهران, ايران , Tarahhomi, Mohammad-Reza hamadan university of medical sciences - School of Medicine - Department of Plastic Surgery, ايران
From page
186
To page
190
Abstract
Objectives: Ectrodactyly-ectodermal dysplasia-clefting syndrome (EEC) is a rare syndrome with features of ectrodactyly, ectodermal dysplasia and cleft lip/palate. This study presents an Iranian case with classic features and oral complications. Case: We report a 20-year old female with all manifestations of this syndrome. The simultaneous presence of these three malformations is extremely rare; the incidence is estimated to be 1.5 per 100.000.000 births. Conclusion: Oral hygiene management of patients with EEC syndrome is important and dental practitioners need to know the oral and dental conditions presenting with this syndrome.
Keywords
Ectrodactyly , Ectodermal dysplasia , Cleft lip , Oral manifestations , Dental complications.
Journal title
Journal of Dental School
Journal title
Journal of Dental School
Record number
2588843
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