Neurofibrosarcoma of the duodenum

A case of neurofibrosarcoma of the second part of the duodenum is reported. The presenting symptom was upper G1 tract bleeding. An emergency pancreaticoduodenectomy was performed to remove a 6 × 8 cm tumour invading the head of the pancreas and the ampulla of Vater. Histopathologically, a low grade malignant neurofibrosarcoma without lymph node invasion was evident. No adjuvant therapy was judged to be necessary. The patient is well and free of disease 5 years following the resection of the neoplasm.