Author/Authors :
Gupta، Veena نويسنده Dept. of Pathology, University of Health Sciences, Rohtak, Haryana , , Sen، Rajeev نويسنده Department of Pathology, Pt. B.D. Sharma Post Graduate Institute of Medical Sciences, Rohtak, Haryana, India , , Batra، Ashima نويسنده Dept. of Pathology, Pt B.D. Sharma University of Health Sciences, Rohtak, Haryana , , Jain، Promil نويسنده Department of Pathology and Gynecology, Pt. B.D Sharma Post Graduate University of Medical Sciences, Rohtak, Haryana, India ,
Abstract :
Primitive neuroectodermal tumors of the kidney are rare tumors representing about
1% of all sarcomas. Extraskeletal primitive neuroectodermal tumors may be found in
the genitourinary tract, the testes, ovaries, uterus, or pancreas. Renal primitive neuroec-
todermal tumors are frequently aggressive and almost 30% of all newly diagnosed cases
present with distant metastases. Surgical intervention, intensive chemotherapeutic
drugs and radiation therapy are the best choices for management.
We discuss the case of a 22-year-old male who presented with a left renal mass. He
underwent nephrectomy followed by histopathological examination. Microscopic and
immunohistochemical examination revealed a primitive neuroectodermal tumor.