Primary atrial fibrosarcoma of the heart

The primary fibrosarcoma of the heart is a rare tumor. There are no exact numbers about its incidence, but even among malignant cardiac tumors, only around 3% are fibrosarcomata. Symptoms are nonspecific with signs of right or left heart failure depending on localization. Diagnosis is thereby often delayed. Primary treatment of choice is surgery, followed by several possible postsurgical adjuvant strategies. Survival is poor with a mean of about 11 months.