Author/Authors :
Januzzi، نويسنده , , James L and Marayati، نويسنده , , Firas and Mehta، نويسنده , , Rajendra H and Cooper، نويسنده , , Jeanna V and OʹGara، نويسنده , , Patrick T and Sechtem، نويسنده , , Udo and Bossone، نويسنده , , Eduardo and Evangelista، نويسنده , , Arturo and Oh، نويسنده , , Jae K and Nienaber، نويسنده , , Christoph A. and Eagle، نويسنده , , Kim A. and Isselbacher، نويسنده , , Eric M، نويسنده ,
Abstract :
Among 1,049 patients diagnosed with aortic dissection in a multinational registry, patients with Marfanʹs syndrome were typically younger and had unique presentations. Despite their younger age at presentation, patients with Marfanʹs syndrome and aortic dissection had a high mortality rate, similar to patients without Marfanʹs syndrome, an older patient cohort. Our data support the importance of aneurysm surveillance and prophylactic surgical intervention for patients with Marfanʹs syndrome to potentially reduce the risk of mortality.
