Author/Authors :
Altun، Ibrahim نويسنده Department of Cardiology, Faculty of Medicine, Mugla Sitki Kocman University, Mugla, Turkey , , Guz، Goksel نويسنده Istanbul University, Faculty of Medicine, Department of Cardiology, Istanbul, Turkey , , Akin، Fatih نويسنده Department of Cardiology, Faculty of Medicine, Mugla Sitki Kocman University, Mugla, Turkey , , Kose، Nuri نويسنده Mugla Sitki Kocman University, Faculty of Medicine, Department of Cardiology, Mugla, Turkey , , Altun، Ilknur نويسنده Mugla Sitki Kocman University, Faculty of Medicine, Department of Radiology, Mugla, Turkey , , Yuksel Gunaydin، Zeki نويسنده Istanbul University, Faculty of Medicine, Department of Cardiology, Istanbul, Turkey , , Sahin، Cem نويسنده Department of Internal Medicine, Faculty of Medicine, Mugla Sitki Kocman University, Mugla, Turkey ,
Abstract :
Multifocal fibrosclerosis is a rare syndrome of unknown cause that is characterized by fibrosis involving multiple organ systems. Definitive diagnosis can only be made based on biopsy findings. In this case, the biopsy specimen of the patient demonstrates pulmonary hyalinated granuloma or sclerosing mediastinitis. There are few reports of multiple fibrosclerosis with heart failure. Here, we reported a case of retroperitoneal fibrosis with massive mediastinal involvement extending to pleura and pericardium causing pleuro- pericardial effusion with dilated cardiomyopathy. Systolic dysfunction was improved and pericardial effusion disappeared with methylprednisolone treatment.
