Author/Authors :
Suleman، M-Irfan نويسنده Division of Pediatric Anesthesia, Arkansas Children’s
Hospital, Arkansas, USA , , Edala، Thejovathi نويسنده Department of Anesthesiology, University of Arkansas for
Medical Sciences, Arkansas, USA , , Abraham، Edwin نويسنده Division of Pediatric Anesthesia, Arkansas Children’s
Hospital, Arkansas, USA , , Siddiqu، M-Saif نويسنده Division of Pediatric Anesthesia, Arkansas Children’s
Hospital, Arkansas, USA ,
Abstract :
Usually presenting in infancy, Leigh’s syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan by which to administer anesthetics remains problematic. We report a male patient with Leigh’s syndrome and a family history suggestive of unknown hypotonia and malignant hyperthermia presenting for dental rehabilitation. Dexmedetomidine with remifentanil can be used with no complication in this senerio