Author/Authors :
Safi، Yaser نويسنده Department of Oral and Maxillofacial Radiology, Dental School, Shahid Beheshti University of Medical Sciences, Tehran, Iran , , Shamloo، Nafise نويسنده Department of Oral and Maxillofacial Pathology, Dental School of Shahid Beheshti University of Medical Sciences, Tehran, Iran , , Heidar، Hossein نويسنده Department of Oral and Maxillofacial Surgery, Tehran
University of Medical Sciences, Tehran, Iran , , Valizadeh، Solmaz نويسنده Department of Oral and Maxillofacial Radiology, School of
Dentistry, Shahid Beheshti University of Medical Sciences, Tehran,
Iran , , Aghdasi، Mohammad Mehdi نويسنده Oral and Maxillofacial Radiology Department, Dental School, Shahid Beheshti University of Medical Sciences, Tehran, Iran Aghdasi, Mohammad Mehdi , Eslami Manouchehri، Maryam نويسنده Department of Oral and Maxillofacial Radiology, School of
Dentistry, Shahid Beheshti University of Medical Sciences, Tehran,
Iran ,
Abstract :
Desmoplastic fibroma (DF) is a rare and locally aggressive
intraosseous tumor with unknown etiology. The mandible is the common
site of involvement in the maxillofacial region. However, it is believed
that DF can arise in any bone of the body. A wide age distribution has
been reported for DF occurrence, extending from birth to the sixth
decade of life, with a peak incidence at 10 to 19 years of age. In this
study, diagnostic and therapeutic management of a 6-year-old girl with a
desmoplastic fibroma of the inferior orbital rim and zygomatic buttress
are discussed. Cone beam computed tomography (CBCT) revealed a mixed
lesion in infraorbital rim, which had ill-defined borders and a straight
thick bony septum inside the lesion. It also involved the zygomatic
process of maxilla and zygomatic bone. According to radiologic concepts,
this rare lesion may mimic fibro-osseous, benign and especially
malignant lesions. Regarding different treatment plans, identification
of this lesion is essential. Furthermore, presence of coarse and
irregular or straight septa along with some imaging criteria for
malignant lesions such as destruction of the cortex, periosteal reaction
and soft tissue invasion would be helpful to differentiate this lesion
from malignant and multilocular benign lesions.
