Author/Authors :
Ghandi، Yazdan نويسنده Amirkabir Hospital, Arak University of Medical Sciences, Arak, IR Iran , , Yousefi Chaichi، Parsa نويسنده Amirkabir Hospital, Arak University of Medical Sciences, Arak, IR Iran , , Sharifi، Mehrzad نويسنده Department of Cardiac Surgery, Rajaie Cardiovascular, Medical and Research Center, Tehran University of Medical Sciences, Tehran, Iran. , , Bolandnazar، Najmeh نويسنده Mafi Military Hospital, Shush, IR Iran ,
Abstract :
Brugada syndrome (BrS) is an autosomal-dominant inherited cardiac arrhythmia that occurs due to sodium channelopathy and increases sudden cardiac death due to episodes of polymorphic ventricular tachyarrhythmia. It is characterized by ST-segment elevation in the right precordial leads and right bundle branch block (RBBB) pattern. We herewith present a case of Brugada syndrome with an unusual presentation. A 2.5-year-old girl with a history of quadriplegic cerebral palsy was admitted due to aspiration pneumonia. Cardiovascular examination and echocardiography was normal. She had a history of surgery for gastro esophageal reflux disease and was under treatment with pantoprazole. Electrocardiogram revealed ST-segment elevation in the right precordial leads (V1 - V3). The patient died during hospitalization due to cardiac arrest before any intervention. The most important feature of Brugada syndrome is clinically suspicion. Therefore it should be considered in cases with uncontrolled seizures, stroke, refractory seizures, recurrent syncope, repeated attacks VT and conduct disorders like RBBB in the absence of structural cardiac and metabolic disorders.
