A Rare Case of Clear Cell Carcinoma of the Parotid Gland in Iran

Salivary gland tumors are rare head and neck lesions. The majority are benign, with only 20% of cases malignant. An epithelial-myoepithelial carcinoma is a rare low-grade malignant salivary and lacrimal gland tumor, which accounts for less than 1% of salivary gland tumors. It mostly involves the parotid gland and affects adults in their sixth and seventh decades. It is usually painless, unless the minor salivary glands are affected. We describe a rare case of a 35-year-old woman who presented with a 1-year-old unilateral painful parotid swelling in December 2014. A complete immunohistochemical study should be considered in cases of malignant salivary gland tumors. To reduce the recurrence rate of these tumors, the optimum therapies are radiotherapy and chemotherapy.