Author/Authors :
malek fatemeh نويسنده , Nazari Shiva نويسنده Pediatric Congenital Hematologic Disorders Research Center, Shahid Beheshti University of Medical Sciences, Tehran, IR Iran , Kazemi Aghdam Maryam نويسنده Pediatric Pathology Research Center, Shahid Beheshti University of Medical Sciences, Tehran, IR Iran , Zavar Navid نويسنده Mofid Children’s Hospital, Pediatric Congenital
Hematologic Disorders Research Center, Shahid Beheshti University of
Medical Sciences, Tehran, Iran , Niafar Sara نويسنده Mofid Children’s Hospital, Shahid Beheshti University of
Medical Sciences, Tehran, Iran , Madani Farhad نويسنده Mofid Children’s Hospital, Pediatric Congenital
Hematologic Disorders Research Center, Shahid Beheshti University of
Medical Sciences, Tehran, Iran , Naderi Sorki Mohammad نويسنده Mofid Children’s Hospital, Pediatric Congenital
Hematologic Disorders Research Center, Shahid Beheshti University of
Medical Sciences, Tehran, Iran
Abstract :
Introduction Rhabdoid Tumor is one of the rare and aggressive
malignant tumors of childhood that was introduced as a subgroup of the
rhabdomyosarcomatoid of the Wilm’s tumor in 1978 at first. Case
Presentation Our patient is a 15-month-old girl referred due to two soft
masses, one in the anterior distal-half part of the left forearm and the
other in the left anterior axillary space with about
5cm × 14cm and 8 -
10cm diameter respectively, and started one month
prior to the study. They were warm, relatively stiff and painless
causing decreased left hand’s movements. In color doppler sonography of
left upper limb, one solid heteroechogenic mass was seen around the
distal left forearm bones and also several hyperechoic ovoid masses were
found (with the greatest diameter of 20 × 14mm).
MRI of left upper limb and finally microscopic and immunohistochemical
study on tissue biopsy sample of anterior mass of left forearm showed
the certain diagnosis. Conclusions Invasiveness, young age of the
patients, limitations of the use of the radiation in this young age and
the tolerance of the chemotheraputic agents in infancy have important
roles in the prognosis of these patients.
