Sydenham Chorea in a Girl with Dextrocardia and Situs Inversus

Sydenham Chorea (SC) is a childhood disease that most frequently occurs after infection with group A B-hemolytic streptococcus species. SC is the most commonly acquired childhood chorea, usually affecting 5 to 15-year-old children. Dextrocardia situs inversus refers to the heart being situated on the right side of the body. We found a case of SC with coexisting dextrocardia and situs inversus, which is rare to our knowledge. A 14-year-old girl was referred to Ali-Ibn-Abiltaleb Hospital due to choreoathetotic movements more in her upper than lower extremities, which impaired her usual function. Antistreptolysin O (ASO) titer was high. Her throat culture was positive for streptococci beta hemolytic. In cardiac study, moderate mitral regurgitation, tricuspid regurgitation, diastolic dysfunction, conus in the Right Ventricle Outlet (RVOT), rightsided aortic arch, dextrocardia, and situs inversus were reported. This was a rare case with SC that had such anomalies.