Author/Authors :
Eshraghi, Bahram Eye Research Center - Farabi Eye Hospital - Tehran University of Medical Sciences, Tehran, Iran , Shadravan, Mahla Department of Ophthalmic Plastic and Reconstructive Surgery - Eye Research Center - Farabi Eye Hospital - Tehran University of Medical Sciences, Tehran, Iran , Aalami, Elham Department of Ophthalmic Plastic and Reconstructive Surgery - Eye Research Center - Farabi Eye Hospital - Tehran University of Medical Sciences, Tehran, Iran , Khalili Pour, Elias Department of Ophthalmic Plastic and Reconstructive Surgery - Eye Research Center - Farabi Eye Hospital - Tehran University of Medical Sciences, Tehran, Iran
Abstract :
Purpose: To describe a patient with Schwartz Jampel vel Aberfeld syndrome (SJS) who underwent orbicularis
oculi myectomy as a treatment for blepharospasm.
Case Report: A 4‑year‑old child with SJS did not respond to an injection of a single dose of botulinum
toxin after one month, so orbicularis myectomy was then performed under general anesthesia. During the
procedure, orbicularis vermiform movements were a useful guide for the extent of myectomy that the patient
needed. He responded very well to this procedure and experienced significant relief of blepharospasm
documented in follow‑up visits for up to 6 months.
Conclusion: Blepharospasm in patients with SJS can be treated with orbicularis oculi myectomy as a good
functional method with faster and durable response in comparison to botulinum toxin injection.
