Title of article :
Spontaneous Scleral Perforation and Optic Nerve Dural Ectasia in Marfan Syndrome
Author/Authors :
Sharifipour, Farideh Department of Ophthalmology - Imam Khomeini Hospital - Ahvaz Jundishapur University of Medical Sciences, Ahvaz , Panahi-Bazaz, Mahmoodreza Department of Ophthalmology - Imam Khomeini Hospital - Ahvaz Jundishapur University of Medical Sciences, Ahvaz , Malekahmadi, Mohammad Department of Ophthalmology - Imam Khomeini Hospital - Ahvaz Jundishapur University of Medical Sciences, Ahvaz , Takhtaeian, Akbar Department of Ophthalmology - Imam Khomeini Hospital - Ahvaz Jundishapur University of Medical Sciences, Ahvaz
Abstract :
Purpose: To report two patients with spontaneous scleral perforation and bleb formation associated
with Marfan syndrome (MFS); which one of them also showed bilateral optic nerve dural ectasia.
Case reports: An 11-year-old girl was referred with progressive myopia. Past medical history was
negative. Slit-lamp examination revealed bilateral scleral thinning and perforation with bleb
formation, shallow anterior chamber (AC), and microspherophakia. Systemic evaluation confirmed
the diagnosis of MFS. B-scan ultrasonography and orbital MRI showed bilateral optic nerve dural
ectasia. A 23-year-old man, known case of MFS, also presented with spontaneous scleral
perforation with bleb formation and microspherophakia. In this case, ancillary tests didn't show
optic nerve dural ectasia. Both patients underwent lensectomy with vitrectomy and iris-fixated
intraocular lens implantation in both eyes.
Conclusion: MFS may be associated with new and rare findings as part of generalized connective
tissue disorder.
Keywords :
Marfan Syndrome , Dural Ectasia , Optic Nerve , Scleral Perforation
Journal title :
Astroparticle Physics
