Optical Coherence Tomography Findings in Idiopathic Perifoveal Telangiectasia

Purpose: To determine the optical coherence tomography (OCT) findings in eyes with idiopathic perifoveal retinal telangiectasis (IPT) Methods: This study is a retrospective review of patient charts, OCT, fundus photography, related to 16 eyes (11 patients). Results: The most consistent finding of idiopathic perifoveal telangiectasia seen in 93.7% of eyes (15 eyes) on OCT was the presence of hyporeflective intraretinal spaces (cysts) in the absence of retinal thickening. Other findings identified in IPT were: loss and disruption of the photoreceptor layer in 87.5% (14 cases), internal limiting membrane draping across the foveola related to an underlying loss of tissue in 25% (4 cases), an abnormal outward disfiguring of outer retinal layers which may be related to outer retinal atrophy in 37.5% (6 cases). Conclusion: The OCT findings in idiopathic perifoveal telangiectasia were characteristic and are helpful for better understanding its pathogenesis and visual function abnormalities.