Author/Authors :
Mottaghi, Kamran Shahid Beheshti University of Medical Sciences, Tehran , Fallahinejadghajari, Rofeideh Shahid Beheshti University of Medical Sciences, Tehran , Sezari, Parisa Shahid Beheshti University of Medical Sciences, Tehran , Kamranmanesh, Mohammadreza Shahid Beheshti University of Medical Sciences, Tehran , Nashibi, Masoud Shahid Beheshti University of Medical Sciences, Tehran
Abstract :
Osteogenesis Imperfecta (OI) is a rare disorder of type 1 collagen with 13 currently identified types attributable to inherited abnormalities in type 1 collagen amount, structure, or processing.OI is a genetic disorder with skeletal, vascular, and soft tissue involvement with different clinical presentations. Since these patients need different surgical procedure in their lifetime, anesthesiologists are involved with their preoperative care and should be familiar with pathogenesis and anesthetic considerations of osteogenesis imperfecta. Here we represent a case of osteogenesis imperfecta, which was candidate for Video Assisted Thoracic Surgery (VATS) and review the literature.
