Xanthogranulomatous Pyelonephritis in a Child

Xanthogranulomatous pyelonephritis (XGPN) is a rare chronic inflammatory disorder in children that results from infection usually associated with longstanding urinary obstruction. There are two morphologic types: diffuse and focal. In the more common diffuse form, the entire kidney is involved. We present a case of diffuse type, in which some foci in the kidney are spared.