Title of article :
A case report of Gorlin–Goltz syndrome as a rare hereditary disorder
Author/Authors :
Sirous , Mehri Associate Professor - Department of Radiology - School of Medicine, Isfahan University of Medical Sciences , Tayari, Nazila Associate Professor - Department of Radiology - School of Medicine, Isfahan University of Medical Sciences
Abstract :
Gorlin–Goltz syndrome is an autosomal dominant and a rare hereditary disease. Diagnosis of this syndrome is based on
major and minor criteria. We report a Gorlin–Goltz syndrome in a 25-year-old male who was presented with progressive
pain of maxilla and mandible over 5 years. The pain was diffuse and compatible with expansile cyst in alveolar
ridges on panoramic radiography. In physical examination, he had coarse face and prognathism. Computer tomography
of face revealed two expansile maxillary and one mandibular cyst. Calcification of entire length in falx and tentorium
were detected in bone window.
Keywords :
Keratogenic Cyst , Falx , Tentorium , Gorlin-Goltz Syndrome
Journal title :
Astroparticle Physics