Extracranial Extrarenal Rhabdoid Tumor: A Case Report

Introduction: Rhabdoid Tumoris one of the rare and aggressive malignant tumors of childhood that was introduced as a subgroup of the rhabdomyosarcomatoid of the Wilm’s tumor in 1978 at first. Case Presentation: Our patient is a 15-month-old girl referred due to two soft masses, one in the anterior distal-half part of the left forearm and the other in the left anterior axillary space with about 5^cm ⨯ 14^cm and 8 - 10^cm diameter respectively, and started one month prior to the study. They were warm, relatively stiff and painless causing decreased left hand’s movements. In color doppler sonography of left upper limb, one solid heteroechogenic mass was seen around the distal left forearm bones and also several hyperechoic ovoid masses were found (with the greatest diameter of 20⨯14^mm). MRI of left upper limb and finally microscopic and immunohistochemical study on tissue biopsy sample of anterior mass of left forearm showed the certain diagnosis. Conclusions: Invasiveness, young age of the patients, limitations of the use of the radiation in this young age and the tolerance of the chemotheraputic agents in infancy have important roles in the prognosis of these patients.