Author/Authors :
Aminimoghaddam, Soheila Department of Gynecology Oncology - Iran University of Medical Sciences , Seifirad, Soroush Endocrinology and Metabolism Research Center (EMRC) - Tehran University of Medical Sciences , Abbasi Dezfouli, Golbahar Department of Gynecology Oncology - Iran University of Medical Sciences , Abbasi, Neda Department of Gynecology Oncology - Iran University of Medical Sciences , Zare Mehrjardi, Ali Department of Pathology - Firoozgar Hospital - Iran University of Medical Sciences , Razavi, Mohsen Department of Gynecology Oncology - Iran University of Medical Sciences , Mahmoudzadeh, Fatemeh Medical Student - Mazandaran University of Medical Sciences
Abstract :
Primitive neuroectodermal tumors are fairly rare in uterus. A case of uterine body primitive neuroectodermal tumor in a 32-year-old Iranian woman is presented. The patient was admitted with abdominal pain and fever and underwent emergency exploratory surgery with total abdominal hysterectomy, bilateral salpingo-oophorectomy, and pelvic lymph node dissection. Posterior wall of the uterus was necrotic and ruptured and a huge tumor disrupted the uterine body. The tumor was strongly positive for CD99, NSE, and chromogranin; No reaction was seen for CD10, CD45 and myogenin. To the best of our knowledge, this is the first report of an uterine body primitive neuroectodermal tumor and the second report of uterine primitive neuroectodermal tumor from Iran.
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