Title of article :
Amyloidosis as a Renal Complication of Chronic Granulomatous Disease
Author/Authors :
Darougar, Sepideh Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Rashid Farokhi, Farin Tehran University of Medical Sciences, Tehran, Iran , Tajik, Shaghayegh Tehran University of Medical Sciences, Tehran, Iran , Baghaie, Nooshin Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Amirmoini, Mehrdad Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Bashardoust, Bahram Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran , Hashemitari, Karen Tehran University of Medical Sciences, Tehran, Iran , Mahdaviani, Alireza Pediatric Respiratory Diseases Research Center - National Institute for Tuberculosis and Lung Disease - Shahid Beheshti University of Medical Sciences, Tehran, Iran
Pages :
5
From page :
228
To page :
232
Abstract :
Chronic granulomatous disease is a rare primary immunodeficiency disorder, which leads to increased susceptibility to recurrent infections and severe inflammatory manifestations. There have been reports regarding different aspects of genitourinary involvement in chronic granulomatous disease, some of which are hydronephrosis, granulomatous cystitis, and glomerulonephritis, but among these complications, amyloidosis is rather rare. We report a patient with chronic granulomatous disease that developed amyloidosis later in the course of the disease.
Keywords :
amyloidosis , genitourinary involvement , chronic granulomatous disorder
Journal title :
Iranian Journal of Kidney Diseases (IJKD)
Serial Year :
2016
Record number :
2519374
Link To Document :
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