Author/Authors :
Vargas, David Salinas Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Sandoval, Jose Antonio Salgado Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Castillo, Luz Dinora Sandoval Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Sánchez, Sandra Antunez Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Uribe, Eduardo Melendez Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Arizmendi, Ramón Alejandro Flores Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Aguilar, Jesús Francisco Montalvo Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City , Chimal, José Luis Aceves Pediatric Cardiology Department, NMC 20 de Noviembre ISSSTE, México City
Abstract :
Clinical presentation of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC)
usually is nonspecific in young, representing a challenge diagnostic. We present an 11-
year-old male patient, with a syncope event and normal ECG in the first medical
assessment. Eight months later, presented a new syncope event, but now with 1st degree
block that evolved to complete AV block in 24 hrs in ECG. In Tertiary Medical Care
Hospital showed sinus arrhythmia with nodal rescues. The echocardiographic
assessment showed dilatation and global hypokinesia in the Right Ventricle. The MR
showed in apex and lateral wall late Gadolinium enhancement indicating fibrosis greater
than 20%. The electrophysiologic assessment showed a low-voltage zone in the RVOT,
normal stimulation between sinus and AV nodes. Was implanted ICD which identified
events of ventricular tachycardia (185 bpm), giving discharges between 21 to 41 Jules,
which were not perceived for the patient. Currently continues under cardiology
surveillance to eventually receive a heart transplant as definitive treatment
