“Benign Tumor with Perivascular Myoid Differentiation”, A Rare Yet Interesting Case Report in a Nine-Month-Old Infant

Introduction: Heart tumors in children are very rare, however in case of presence, they may cause significant morbidity. Case Report: We present a nine-month-old female infant who was admitted to the emergency ward due to severe tachypnea. Echocardiography showed a huge echogenic mass in the right atrium occupying almost half of its cavity. It was originated from the roof of RA and would herniate to the right ventricle during diastole causing tricuspid valve stenosis. The excised specimen was similar to a cardiac myxoma. Microscopically, a myxoid background was seen with foci of spindle cell proliferation. Further study of the tumor showed that it was of smooth muscle origin. After nine months of follow-up from the surgery date, she was healthy. Conclusions: Considering benign nature of the tumor and its derivation from smooth muscle, it is appropriate to designate it “Benign Tumor with Perivascular myoid differentiation”. This is a rare, interesting entity which conforms to our findings.