Case Report: Unilateral Pulmonary Artery Agenesis Presenting with Massive Hemoptysis

Background: Congenital unilateral absence of a pulmonary artery is a rare anomaly most frequently accompanied by other cardiovascular anomalies. It is usually diagnosed during childhood and effectively treated surgically by doing a pneu-monectomy. Case Report: A young adult with right pulmonary artery agenesis, who presented in November 2011 to Aseer Central Hospital with massive hemoptysis. He was treated successfully with arterial embolization, as the definitive management plan was an elective pneumonectomy after referral to an expert specialized center for the latter form of treatment. Conclusion: Pulmonary artery agenesis, needs to be considered as a cause of recurrent hemoptysis, especially in a patient with decreased unilateral lung volume. Such patients should be strongly considered for undergoing a pulmonary angiography for confirming this rare pulmonary vascular malformation.