Title of article
Partial Internal Biliary Diversion in Progressive Familial Intrahepatic Cholestasis: Introduction of a New Approach
Author/Authors
Zhao, Ning Affiliated Hospital of China Medical University - Shengjing Hospital - Department of Infectious Diseases, China , Wang, Xue-Lian Affiliated Hospital of China Medical University - Shengjing Hospital - Department of Infectious Diseases, China , Gu, Qiu-Hong Affiliated Hospital of China Medical University - Shengjing Hospital - Department of Infectious Diseases, China , Huang, Fen Affiliated Hospital of China Medical University - Shengjing Hospital - Department of Infectious Diseases, China , Zheng, Wei Department of Pathophysiology, China Medical University, China , Li, Zhi-Wei Affiliated Hospital of China Medical University - Shengjing Hospital - Department of Infectious Diseases, China
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Abstract
Introduction: Facilitation of biliary salts secretion represents the mainstay of treatment for progressive familial intrahepatic cholestasis (PFIC). The purpose of this study was to introduce a new approach for the treatment of progressive familial intrahepatic cholestasis (PFIC) to avoid ostoma.Case Presentation: An 11-year-old girl with the diagnosis of PFIC underwent cholecystoappendicostomy with myotomy operation. Because of anastomosis stricture, she was reoperated with cholecystojejunocolic anastomosis and intussuscepted valve surgery. She was followed for 9 months. Despite disappointing outcomes of internal drainage with cholecystoappendicostomy, results of cholecystojejunocolic anastomosis with intussuscepted valve surgery were promising. Discussion: The cholecystojejunocolic anastomosis with intussuscepted valve surgery could be considered as a forthcoming approach in the treatment of intrahepatic cholestasis.
Keywords
Cholestasis , Billiary Diversion , Pruritus
Journal title
Hepatitis Monthly
Journal title
Hepatitis Monthly
Record number
2557886
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