An impressive image of unilateral pulmonary artery agenesis associated with coronary collateralization in an adult

Isolated unilateral absence of pulmonary artery (UAPA) is a very rare congenital anomaly in adults. The prevalence of this anomaly is about 1 in 200.000 live births. It is usually diagnosed in early childhood and the average age of patients with the condition is 14 years (0–58 years) (1, 2). Clinical symptoms of the patient, anatomical variation of the pulmonary artery (PA), and additional cardiovascular anomalies together with their associated collateral circulation and pulmonary hypertension (PHT) are important factors to consider in the choice of treatment (3).