HYPOKALEMIA WITH RENAL TUBULAR ACIDOSIS TYPE I AS AN INITIAL PRESENTATION OF PRIMARY SJOGREN’S SYNDROME

Renal involvement either interstitial nephritis or glomerulonephritis have been seldom noticed in isolated cases of primary Sjogren’s syndrome (pSS). In pSS, renal involvement is primarily due to a monolymphocytic tubulointerstitial nephritis (TIN) characterised by a predominance of T lymphocyte subsets and manifested by renal tubular dysfunction. In this instance, we describe a case of primary Sjogren’s syndrome presenting with hypokalemia and renal tubular acidosis type I including relevant positive and negative history and laboratory evidence of renal dysfunction. This case shows that primary Sjogren’s syndrome may present with systemic manifestations other than classical one