Author/Authors :
Baghaei, R. tehran university of medical sciences tums - Rajaie Cardiovascular, Medical and Research Center, تهران, ايران , Noohi, F. tehran university of medical sciences tums - Rajaie Cardiovascular, Medical and Research Center, تهران, ايران , Tootoonchi, Z. tehran university of medical sciences tums - Rajaie Cardiovascular, Medical and Research Center, تهران, ايران , Mohebbi, B. tehran university of medical sciences tums - Rajaie Cardiovascular, Medical and Research Center, تهران, ايران , Azarshab, A. tehran university of medical sciences tums - Rajaie Cardiovascular, Medical and Research Center, تهران, ايران
Abstract :
Severe cardiovascular disorders, including aortic dissection and aneurismal dilation of the aorta, are the main life-threatening complications of the Marfan syndrome1. Approximately two thirds of individuals who have this syndrome have chest wall deformities such as pectus excavatum or pectus carinatum2. When a patient with pectus excavatum needs aortic surgery, the surgeon may face a major clinical challenge in choosing the optimal surgical approach3. We present a case of the Marfan syndrome with severe pectus excavatum who underwent aortic surgery