Title of article :
Overlapping syndromes: keratosis follicularis spinulosa decalvans with overlapping features of ichthyosis follicularis with alopecia and photophobia
Author/Authors :
Khan, Ikramullah Pakistan Institute of Medical Sciences - Department of Dermatology, Pakistan , Ahmed, Sayed Afaq Pakistan Institute of Medical Sciences - Department of Dermatology, Pakistan , Qadeer, Ambreen Pakistan Institute of Medical Sciences - Department of Dermatology, Pakistan
Abstract :
We report a case of a 20-year-old male who presented in our dermatology clinic with congenital alopecia totalis, ectropion, bilateral cataract, follicular prominence, plantar keratoderma, ichthyosis on legs, cheilitis, xerosis and photophobia. He had overlapping features of both keratosis follicularis spinulosa decalvans and ichthyosis follicularis with alopecia and photophobia. Or was it a different entity altogether?
Keywords :
Keratosis follicularis spinulosa decalvans , ichthyosis follicularis , alopecia , photophobia
Journal title :
Journal of Pakistan Association of Dermatologists
Journal title :
Journal of Pakistan Association of Dermatologists