Author/Authors :
Nasir, Abdulrasheed A. University of Ilorin Teaching Hospital - Department of Surgery, Paediatrics Surgery Division, Nigeria , Abdur-Rahman, Lukman O. University of Ilorin Teaching Hospital - Department of Surgery, Paediatrics Surgery Division, Nigeria , Ibrahim, Kazeem O. O. University of Ilorin Teaching Hospital - Department of Pathology, Paediatrics Surgery Division, Nigeria , Adegoke, Muideen A. University of Ilorin Teaching Hospital - Department of Surgery, Paediatrics Surgery Division, Nigeria , Afolabi, Joselp K. University of Ilorin Teaching Hospital - Department of Paediatrics, Nigeria , Adeniran, James O. University of Ilorin Teaching Hospital - Department of Surgery, Paediatrics Surgery Division, Nigeria
Abstract :
Neurofibromatosis is a common inherited autosomal dominant disease, but genitourinary neurofibroma is rare. The unpredictable nature of neurofibromas has a serious impact on the quality of life of patients, and their management is challenging for clinicians. We present a 9-year-old girl with plexiform neurofibroma of genitourinary system associated with pulmonary hypertension, masquerading as sacrococcygeal teratoma. Intraoperative finding and histological examination of the resected tumor confirmed the diagnosis.
Keywords :
Genitourinary , plexiform neurofibroma , pulmonary hypertension , sacrococcygeal tumor
