Primary localized AA type amyloidosis of the renal pelvis, ureter and bladder

We report an unusual variant, amyloid AA, of an already unusual condition, primary localized amyloidosis of the renal pelvis. Our patient is a 68-year-old man with a space-occupying lesion in left renal pelvis found by CT. He was suspected of having malignancy before ureteroscopy. Specimens were taken from the lesion site and pathological result was amyloidosis. No treatment has been given to him for the primary pelvic amyloidosis. New lesions were found in the bladder 10 months later and in the left ureter 21 months later, respectively. It is the first case of primary renal pelvic AA type amyloidosis in which the patient has been monitored for the progress of lesions in renal pelvis, ureter and bladder.