Author/Authors :
Li, Hui-Yan Zhejiang University - School of Medicine, First Affiliated Hospital - Ophthalmology, China , Cui, Hong-Guang Zhejiang University - School of Medicine, First Affiliated Hospital - Ophthalmology, China , Zheng, Xue-Yong Zhejiang University - School of Medicine, Sir Run Run Shaw Hospital - General Surgery, China , Ren, Guo-Ping Zhejiang University - School of Medicine, First Affiliated Hospital - Pathology, China , Gu, Yang-Shun Zhejiang University - School of Medicine, First Affiliated Hospital - Ophthalmology, China
Abstract :
Rosai–Dorfman disease (RDD) is rare and characterized by histiocytic proliferation and massive cervical lymphadenopathy. About 40% of patients have extra-nodal involvement. Ophthalmic involvement is seen in 10% of cases. A case of orbital Rosai Dorfman disease in a 58 years old woman is presented here, who was misdiagnosed as orbital inflammatory disease initially. The patient did not respond to a course of oral prednisolone. Then complete surgical excision of the mass was performed and the histopathological examination was consistent with a diagnosis of RDD.
