Author/Authors :
Koley, Sankha Jawaharlal Nehru Medical College - Department of Dermatology, India , Salodkar, Atul Jawaharlal Nehru Medical College - Department of Dermatology, India , Gupta, Sumit Jawaharlal Nehru Medical College - Department of Dermatology, India , Bhanke, Arvind Jawaharlal Nehru Medical College - Department of Pathology, India , Ujawane, Ashish Jawaharlal Nehru Medical College - Department of Medicine, India , Bisati, Shazia Jawaharlal Nehru Medical College - Department of Dermatology, India
Abstract :
Ichthyosis bullosa of Siemens (IBS) is a rare disease characterized by superficial blistering, mild epidermal hyperkeratosis over flexural areas and characteristic mauserang phenomenon (moulting).We report an interesting case of IBS in a mentally retarded hypothyroid patient who did not give any history of blistering. Histological examination of specimen from margin of an area exhibiting mauserung phenomenon revealed epidermolytic hyperkeratosis in granular and upper spinous layers. In situations where proper clinical history cannot be elicited, the histopathological findings have paramount importance.
