Title of article :
GORLIN-GOLTZ SYNDROME
Author/Authors :
Pakfetrat, Atessa mashhad university of medical sciences - Faculty of Dentistry - Dental Research Center, ايران , Falaki, Farnaz mashhad university of medical sciences - Faculty of Dentistry - Dental Research Center, ايران , Mahmoodabadi, Reza Zare mashhad university of medical sciences - Faculty of Dentistry - Dental Research Center, ايران , Saghafi, Shadi mashhad university of medical sciences - Faculty of Dentistry - Dental Research Center, ايران
Abstract :
We report a case of Gorlin-Goltz syndrome in a 21-year-old man. Gorlin-Goltz syndrome (basal cell nevus syndrome) is an infrequent hereditary disease with its prevalence varying from 1/ 57,000 to 1/250,000.It is principally characterized by a wide range of developmental abnormalities. Main clinical manifestations include multiple odontogenic keratocysts of the jaws, facial basal cell carcinomas and skeletal anomalies. The prevalence varies from 1/57,000 to 1/250,000.
Keywords :
Gorlin , Goltz Syndrome , Nevoid Basal Cell Carcinoma Syndrome (NBCCS) , Basal Cell Nevus Syndrome , Odontogenic Keratocyst , Basal Cell Carcinoma
Journal title :
Pakistan Journal of Medical Sciences
Journal title :
Pakistan Journal of Medical Sciences
