Title of article :
Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Adenitis Syndrome: Report of Three Cases
Author/Authors :
Taş, Derya Babuş Erciyes Üniversitesi - Tıp Fakültesi - Pediatri Anabilim Dalı, Türkiye , Poyrazoğlu, M. Hakan Erciyes Üniversitesi - Tıp Fakültesi - Çocuk Nefroloji Bilim Dalı, Türkiye , Tülpar, Sebahat Erciyes Üniversitesi - Tıp Fakültesi - Çocuk Nefroloji Bilim Dalı, Türkiye , Yel, Sibel Erciyes Üniversitesi - Tıp Fakültesi - Çocuk Nefroloji Bilim Dalı, Türkiye , Baştuğ, Funda Erciyes Üniversitesi - Tıp Fakültesi - Çocuk Nefroloji Bilim Dalı, Türkiye , Gündüz, Zübeyde Erciyes Üniversitesi - Tıp Fakültesi - Çocuk Nefroloji Bilim Dalı, Türkiye , Düşünsel, Ruhan Erciyes Üniversitesi - Tıp Fakültesi - Çocuk Nefroloji Bilim Dalı, Türkiye
Abstract :
Periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome, which was first described in 1987 by Marshall et al. and is characterized by periodic fever, aphthous stomatitis, pharyngitis and cervical lymphadenopathy is an autoinflammatory disease. This syndrome usually occurs in patients under 5 years and has a benign course. In this study we presented three children with PFAPA syndrome. All patients received multiple antibiotic therapies because of a diagnosis of upper respiratory tract infection and all three patients had dramatic responses to oral corticosteroid. With this case report, we aimed to draw attention to PFAPA syndrome because we believe that PFAPA is more common than estimated and is often misdiagnosed
