Author/Authors :
Iezzi, Federica Department of Paediatric and Congenital Cardiac Surgery and Cardiology - Azienda Ospedaliero-Universitaria Ospedali Riuniti Ancona “Umberto I, Italy , Quarti, Andrea Department of Paediatric and Congenital Cardiac Surgery and Cardiology - Azienda Ospedaliero-Universitaria Ospedali Riuniti Ancona “Umberto I, Italy , Surace, Chiara Department of Paediatric and Congenital Cardiac Surgery and Cardiology - Azienda Ospedaliero-Universitaria Ospedali Riuniti Ancona “Umberto I, Italy , Pozzi, Marco Department of Paediatric and Congenital Cardiac Surgery and Cardiology - Azienda Ospedaliero-Universitaria Ospedali Riuniti Ancona “Umberto I, Italy
Abstract :
Adrenocortical carcinoma is a rare malignancy. Due to late diagnosis and no adequate effective adjuvant treatment, prognosis
remains poor. Only approximately 30% of these malignancies are confined to the adrenal gland when they are diagnosed, as these
tumors tend to be found years after their genesis. Cardiac involvement of adrenal carcinoma is very rare. We report a rare case of a
7-year-old female with right adrenal cortical carcinoma, involving the right-side heart.