Pulmonary Metastases from an Undifferentiated EmbryonalSarcoma of the Liver: A Case Report and Review

Undifferentiated embryonal sarcoma of the liver (UESL) is a rare malignant hepatic tumor that occurs primarily in children. Only alimited number of cases have been reported in the literature due to low incidence of one per million, and reports of metastatic lesionof UESL are even rarer. We hereby describe the case of a 13-year-old male who presented with a palpable mass with imagingfindings suggestive of a large complex tumor in the right lobe of the liver. He underwent extended right hepatectomy followedby adjuvant chemotherapy. The tumor was confirmed to be UESL by postoperative pathology and immunohistochemicalstaining analysis. Four years later, surveillance imaging revealed a small lung nodule in the left lower lobe. Complete removal ofthe lung tumor by wedge resection was performed, and a histological diagnosis of metastatic UESL was made. The patient alsoreceived postoperative adjuvant chemotherapy and is currently in a good general condition and tumor-free in the present eight-month period. This case is presented with emphasis on clinicopathological and immunohistochemicalfindings of the primaryUESL and lung metastases with the aim of collecting more data and expanding our understanding of this rare malignancy