Author/Authors :
Grzybowska-Szatkowska, L Chair and Department of Oncolog y - Medical University of Lublin - Lublin, Poland , Bilski, M Chair and Department of Oncolog y - Medical University of Lublin - Lublin, Poland , Cisek, P Chair and Department of Oncolog y - Medical University of Lublin - Lublin, Poland , Surdyka, D Radiation erapy Department - Lublin Oncological Center - Lublin, Poland , Pa ́snik, I Chair and Department of Clinical Pathomorphology - Medical University of Lublin - Lublin, Poland , Bilska, M Gynecological Oncology and Gynecology Clinic - Independent Public Clinical Hospital No.1 in Lublin - Lublin, Poland , Korona, P Radiation erapy Department - Lublin Oncological Center - Lublin, Poland , Szumiło, J Chair and Department of Clinical Pathomorphology - Medical University of Lublin - Lublin, Poland
Abstract :
Spleen sarcoma is one of the most rare soft tissue malignancies. +e annual incidence is 0.14–0.25/1,000,000 and the average age ofdiagnosis is 50 to 73 years. +e incidence of this cancer has been increasing. Treatment of choice is surgical splenectomy, whichrarely gives good results due to the aggressive course of the disease as well as the high potential for metastasis. Overall survival inprimary spleen sarcomas as described by various authors is between 4 and 14 months. 80% of patients after spleen rupture do notsurvive 6 months. We report the case of a 42-year-old male diagnosed with spleen angiosarcoma. +e patient underwent surgery inan emergency mode because of rapid rupture of the organ. Due to positive surgical margins, he underwent adjuvant radio-chemotherapy followed by chemotherapy. Overall survival time was relatively long (23 months). +e international guidelinesprovide information based on limited data. +e role of postoperative radiotherapy in angiosarcomas remains controversial.Postoperative radiotherapy may increase local disease control, especially after nonradical operation, but this does not translateinto improvement in overall survival time of these patients. +e case shows that adjuvant radiotherapy as part of cancer treatmentstrategy may prolong the overall survival.
Keywords :
Adjuvant Radiochemotherapy , 23-Month Overall Survival Time , Patient , Surgery due Splenic Hemangiosarcoma Rupture
