Author/Authors :
Ahmad, H.R Haematology/Oncology Unit - Department of Paediatrics - Ahmadu Bello University/Teaching Hospital - Zaria, Nigeria , Faruk, J.A. Haematology/Oncology Unit - Department of Paediatrics - Ahmadu Bello University/Teaching Hospital - Zaria, Nigeria , Solomon, A Haematology/Oncology Unit - Department of Paediatrics - Ahmadu Bello University/Teaching Hospital - Zaria, Nigeria , Bugaje, M.A. Nephrology Unit - Department of Paediatrics - Ahmadu Bello University/Teaching Hospital - Zaria, Nigeria , Akuse, R.M. Nephrology Unit - Department of Paediatrics - Ahmadu Bello University/Teaching Hospital - Zaria, Nigeria , Samaila, M.O.A. Department of Pathology - Ahmadu Bello University/Teaching Hospital - Zaria, Nigeria
Abstract :
Malignancies have been reported to occur in people with sickle cell disease. Renal medullary carcinoma (RMC), also taggedseventh sickle cell nephropathy, is an aggressive cancer seen almost exclusively in people with sickle cell disease with more than160 cases reported worldwide, but only few cases were reported in patients with sickle cell anaemia (HBSS) and from Nigeria.Sarcomatoid renal cell carcinoma is a renal tumour of any histologic variant containing foci of high-grade malignant spindle cells.We report an adolescent girl with sickle cell anaemia (HBSS) who presented with left renal tumour, histology of which con7rmeda diagnosis of sarcomatoid renal cell carcinoma (sRCC). Surgical debulking and palliative care with chemotherapy were given, andshe demised 10 months after. )e rarity of the case and challenges of managing a cancer in the background of a chronichaematologic disorder are highlighted
Keywords :
Sarcomatoid Renal Cell Carcinoma , Adolescent , Sickle Cell Anaemia , HBSS , RMC , sRCC
