Author/Authors :
Aghaei Moghadam, Ehsan Children’s Medical Center - Pediatrics Center of Excellence, Tehran, Iran , Aslani, Nahid Department of Pediatrics - Isfahan University of Medical Science, Isfahan, Iran , Mojtabavi, Helia Children’s Medical Center - Pediatrics Center of Excellence, Tehran, Iran , Larti, Farnoosh Children’s Medical Center - Pediatrics Center of Excellence, Tehran, Iran , Ghamari, Azin Growth and Development Research Center -Tehran University of Medical Science, Tehran, Iran , Ziaee, Vahid Children’s Medical Center - Pediatrics Center of Excellence, Tehran, Iran
Abstract :
Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to
mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare
annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which,
aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a
rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm.
GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents.
Keywords :
Giant Thrombosis , Artery Aneurysm , Granulomatosis , Polyangiitis