Author/Authors :
Ahmad Jan, Iftikhar Departments of Pediatric Surgery - Zayed Military Hospital, Abu Dhabi, United Arab Emirates , AlKaabi, Saif Khalfan Departments of Pediatric Medicine - Zayed Military Hospital, Abu Dhabi, United Arab Emirates , Al Mughadam, Awadh Departments of Anesthesia - Zayed Military Hospital, Abu Dhabi, United Arab Emirates , Murthy D, Sreenivas Departments of Pediatric Surgery - Zayed Military Hospital, Abu Dhabi, United Arab Emirates , AlHamoudi, Basmah Departments of Pediatric Surgery - Zayed Military Hospital, Abu Dhabi, United Arab Emirates
Abstract :
Glanzmann's thrombasthenia (GT) is a rare autosomal recessive disorder in which the platelets have anomalies of fibrinogen receptors causing bleeding tendencies. The disease usually presents with mucosal bleeding, petechial haemorrhages or gastrointestinal (GI) bleeding. Only sporadic cases of intussusception or duodenal haematoma have been reported with GT. We present a case of 5-year-old girl admitted with non-bilious vomiting, watery diarrhoea and abdominal pain. She is a known patient of Glanzmann's thrombasthenia.
Keywords :
Complications , duodenal haematoma , Glanzmann thrombasthenia , intussusception