Title of article :
Collagenofibrotic Glomerulopathy: Report a Rare Case
Author/Authors :
Agarwal, Rakesh Institute of Post-Graduate Medical Education and Research and Seth Sukhlal Karnani Memorial Hospital - Kolkata - India , Baid, Rashmi Lilavati Hospital & Research Centre - Mumbai - India , Mukhopadhyay, Jotideb Institute of Post-Graduate Medical Education and Research and Seth Sukhlal Karnani Memorial Hospital - Kolkata - India
Abstract :
Collagenofibrotic glomerulopathy is a rare clinical entity with fewer than 40 cases reported worldwide. We describe a case of adult onset nephrotic syndrome with partial villous atrophy of the intestine who was diagnosed with this rare entity. Collagenofibrotic glomerulopathy is characterized by subendothelial and mesangial collagen type III deposition and increased procollagen III peptide levels. Extra renal involvement has been described in the form of hypertension, anemia and microangiopathic hemolytic anemia but villous atrophy has not been associated with this condition so far, possibly reflecting the paucity of literature. We describe this case and review the condition in this report.
Keywords:
Keywords :
Collaagenofibrotic glomerulopathy , Nephrotic syndrome
Journal title :
Archives of Iranian Medicine