Segmental neurofibromatosis (a rare variant of a common genodermatosis): report of two cases

Segmental neurofibromatosis is a rare variant of neurofibromatosis in which the lesions are confined to one segment or dermatome of the body. They resemble classical neurofibromas in their morphology, histopathology. However, systemic associations are usually absent. We report two cases representing with segmental distribution of neurofibromas on localized areas of the skin over back and chin respectively. They had negative family history and were lacking any systemic involvement.