Oral manifestations of lamellar ichthyosis: A rare case report and review

Ichthyosis is a heterogeneous family of hereditary disorders mostly characterized by the accumulation of hyperkeratotic scales. Although these disorders affect tissues of epidermal origin, there is little evidence regarding the involvement of oral and dental structures in ichthyosis. Perioral tissues, however, are frequently affected both by disease and drugs used for treatment. A case report of dental involvement in lamellar ichthyosis is presented and the dental management is discussed.