Author/Authors :
Alizadeh-Sani, Zahra tehran university of medical sciences tums - Shaheed Rajaei Cardiovascular, Medical and Research Center, تهران, ايران , Madadi, Shabnam tehran university of medical sciences tums - Shaheed Rajaei Cardiovascular, Medical and Research Center, تهران, ايران , Sadeghpour, Anita tehran university of medical sciences tums - Shaheed Rajaei Cardiovascular, Medical and Research Center, تهران, ايران , Khajali, Zahra tehran university of medical sciences tums - Shaheed Rajaei Cardiovascular, Medical and Research Center, تهران, ايران , Golnari, Pedram tehran university of medical sciences tums - Shaheed Rajaei Cardiovascular, Medical and Research Center, تهران, ايران , Kiavar, Majid tehran university of medical sciences tums - Shaheed Rajaei Cardiovascular, Medical and Research Center, تهران, ايران
Abstract :
Left ventricular non-compaction cardiomyopathy is a rare congenital cardiomyopathy that affects both children and adults. Since the clinical manifestations are not sufficient to establish diagnosis, echocardiography is the diagnostic tool that makes it possible to document ventricular non-compaction and establish prognostic factors. We report a 47-year-old woman with a history of dilated cardiomyopathy with unknown etiology. Echocardiography showed mild left ventricular enlargement with severe systolic dysfunction (EF = 20-25%). According to cardiac magnetic resonance imaging findings non-compaction left ventricle with hypertrophic cardiomyopathy was considered, and right ventricular septal biopsy was recommended. Right ventricular endomyocardial biopsy showed moderate hypertrophy of cardiac myocytes with foci of myocytolysis and moderate interstitial fibrosis. No evidence of infiltrative deposition was seen.
