Author/Authors :
chin, ken min national university of singapore - yong loo lin school of medicine, Singapore , ho, woon yang singapore general hospital - department of general surgery, Singapore , lim, kiat hon tony singapore general hospital - department of pathology, Singapore , chung, yaw fui alexander duke-national university of singapore (nus) - medical school, Singapore , chung, yaw fui alexander singapore general hospital - department of general surgery, department of hepatopancreatobiliary and transplant surgery, Singapore , lee, ser yee duke-national university of singapore (nus) - medical school, Singapore , lee, ser yee singapore general hospital - department of general surgery, department of hepatopancreatobiliary and transplant surgery, Singapore
Abstract :
Follicular dendritic cell sarcoma (FDCS) of the liver is an extremely rare disease, accounting for a mere 0.4% of all soft tissue sarcomas. FDCS most commonly involves lymph nodes but also affects extranodal sites such as the gastrointestinal system, oral cavity, liver, spleen and pancreas, albeit less commonly. It is widely considered a low-to-intermediate grade malignancy. We report a case of FDCS with metachronous involvement of the liver, small intestines and spleen, its imaging, histological findings and its management.
Keywords :
Follicular dendritic cell sarcoma (FDCS) , liver , extra , nodal
